Korean J Dermatol.  2005 Nov;43(11):1513-1517.

A Case of Large Vascular Plexiform Neurofibroma Associated with Giant Cafe-au-lait Patch and Scoliosis

Affiliations
  • 1Department of Dermatology, College of Medicine, Korea University, Seoul, Korea.
  • 2Department of Dermatology, College of Medicine, The Catholic University of Korea, Seoul, Korea.

Abstract

Plexiform neurofibromas are benign proliferations arising from the peripheral nerves and represent one of the diagnostic features of neurofibromatosis type 1. We present a case of a 14-year-old boy, who had large vascular neurofibromatous elephantiasis associated with a giant cafe-au-lait patch on his lateral aspect of the left hemithorax. Although he had no perceptible symptoms, radiologic examination revealed mild thoracic scoliosis with left side convexity. Our treatment of the skin lesion was one-stage palliative tumor debulking.

Keyword

Giant caf?-au-lait patch; Plexiform neurofibroma; Scoliosis

MeSH Terms

Adolescent
Elephantiasis
Humans
Male
Neurofibroma, Plexiform*
Neurofibromatosis 1
Peripheral Nerves
Scoliosis*
Skin
Full Text Links
  • KJD
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr