J Korean Soc Radiol.  2015 Oct;73(4):252-258. 10.3348/jksr.2015.73.4.252.

A Case Report of an Unusual Type of Choledochal Cyst with Choledocholithiasis: Saccular Dilatation of the Confluent Portion of Both Intrahepatic Ducts

Affiliations
  • 1Department of Radiology, Eulji University Hospital, Daejeon, Korea. orionphil@hotmail.com

Abstract

A choledochal cyst is a rare congenital anomaly of the biliary system manifested as the cystic dilatation of bile ducts, usually occurring in the common bile duct. Here, we describe an unusual type of choledochal cyst in a 45-year-old male that did not fit into the most widely accepted Todani classification of these cysts. The lesion mimicked duplication anomalies of the gallbladder and was finally diagnosed as a choledochal cyst involving the confluent portion of both intrahepatic ducts.


MeSH Terms

Bile Ducts
Biliary Tract
Choledochal Cyst*
Choledocholithiasis*
Classification
Common Bile Duct
Dilatation*
Gallbladder
Humans
Male
Middle Aged

Figure

  • Fig. 1 Axial (A, B), coronal (C), and sagittal (D) views of a contrast-enhanced abdominal CT showing a round cystic lesion (arrow) with multiple internal calcified stones, at the porta hepatis (just superior to the gallbladder). Gallbladder (asterisk) showing a calcified stone (arrowhead) without mural thickening as an inflammation.

  • Fig. 2 Abdominal ultrasonography showing a thin-walled cystic lesion (arrows) abutting the gallbladder (asterisk) near the porta hepatis. It contains multiple echogenic foci with posterior shadowing, suggesting calcified stones. The lesion does not show the anatomical layering of its wall that is detected in the gallbladder.

  • Fig. 3 Magnetic resonance cholangiopancreatography images. A. Maximal intensity projection image showing the gallbladder (asterisk) and a round cystic lesion (arrows) in the confluent portion of both intrahepatic ducts (IHDs). There is no anomalous pancreaticobiliary ductal union. A schematic representation is also shown (right). B, C. Left IHD (arrow in B) and right IHD (arrow in C) directly arose from the cyst, which is representative of the choledochal cyst. Multiple filling defects suggesting cholelithiasis and choledocholithiasis are shown in the gallbladder and choledochal cyst.

  • Fig. 4 Endoscopic retrograde cholangiopancreatography shows sequential contrast filling of the common bile duct, cystic lesion, and both intrahepatic ducts (IHDs) (arrows), which are consistent with a choledochal cyst occupying a confluent portion of both IHDs.


Reference

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