Korean J Urol.  2007 May;48(5):561-563. 10.4111/kju.2007.48.5.561.

Functional Paraganglioma of the Pelvic Cavity

• Lee SW
• Kim DS
• Cho HD
• Lee CH
• Jeon YS
• Lee NK

• KMID: 2061266
• DOI: http://doi.org/10.4111/kju.2007.48.5.561

Abstract

Paraganglioma is one of the pheochromocytomas, and this arises in the extra-adrenal tissue. It is a rare tumor of neural crest origin; it accounts for at least 10% of all the pheochromocytomas. Paragangliomas produce catecholamines and on the basis of this, they are classed as either functional or nonfunctional. We report here on our experience with laparoscopic removal of functional paragangliomas of the pelvic cavity and we include a brief review of literatures.

Keyword

Paraganglioma, extra-adrenal; Laparoscopy; Pelvis

MeSH Terms

Catecholamines
Laparoscopy
Neural Crest
Paraganglioma*
Paraganglioma, Extra-Adrenal
Pelvis
Pheochromocytoma
Catecholamines

Figure

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  Fig. 1 Horizontal section of the computed tomography shows a 3.4×2.3cm sized, well defined, oval-shaped enhanced mass in the extraperitoneal portion of the right pelvic cavity.

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  Fig. 2 Laparoscopic view of the pelvic mass (M) and the feeding vessel (arrow) being ligated by using clips.

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  Fig. 3 (A) This shows the "zellballen" pattern of the monotonous tumor cells with a moderate amount of cytoplasm, and the intervening capillaries (H&E, ×200). (B) Immunohistochemistry reveals the S-100 protein-positive sustentacular cells (×200).

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