Skip Navigation
Skip to contents

Obstet Gynecol Sci.  2015 Sep;58(5):427-430. 10.5468/ogs.2015.58.5.427.

Massive hemoperitoneum due to a ruptured corpus luteum cyst in a patient with congenital hypofibrinogenemia

Affiliations
  • 1Department of Obstetrics and Gynecology, Institute for Medical Sciences, Chonbuk National University Medical School, Jeonju, Korea. obgyn2001@jbnu.ac.kr

Abstract

Congenital afibrinogenemia/hypofibrinogenemia is a rare inherited hematologic disorder in which a patient lacks or has insufficient level of fibrinogen, the blood coagulation factor I. The incidence of this uncommon disease is 1 to 2 per 1 million individuals. Hence, massive hemoperitoneum caused by ovulation in a woman with congenital afibrogenemia is also a very rare clinical condition. Massive hemoperitoneum usually presents as acute abdominal pain with potential findings of peritonitis including abdominal distention, hypotension and tachycardia with critical consequences. We performed emergent endoscopic surgery for hemoperitoneum caused by a ruptured corpus luteum cyst in a patient with congenital hypofibrinogenemia. To the best of our knowledge, this was the first case report of such treatment in Korea.

Keyword

Afibrinogenemia; Hemoperitoneum; Hypofibrinogenemia congenital; Ovarian cysts; Rupture

MeSH Terms

Abdominal Pain
Afibrinogenemia
Corpus Luteum*
Female
Fibrinogen
Hemoperitoneum*
Humans
Hypotension
Incidence
Korea
Ovarian Cysts*
Ovulation
Peritonitis
Rupture
Tachycardia
Fibrinogen
Full Text Links
  • OGS
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2026 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr