Brain Tumor Res Treat.  2013 Oct;1(2):121-123. 10.14791/btrt.2013.1.2.121.

An Ependymal Cyst in Cerebello-Pontine Angle Presenting with Syncope

• Park BJ
• Kim YI
• Jeun SS
• Lee YS

• KMID: 2048488
• DOI: http://doi.org/10.14791/btrt.2013.1.2.121

Abstract

Intracranial ependymal cysts are rare, congenital, benign lesions. These commonly occur in the supratentorial regions and usually generate no symptoms. The cerebellopontine angle (CPA) is an extremely rare site for ependymal cysts. Furthermore, there are no previous reports of CPA ependymal cysts related to syncope. We report a case of ependymal cyst in the left CPA with syncope. The patient underwent a cardiologic evaluation for syncope after admission, but there were no definite cardiologic abnormal findings. He underwent fenestration into the subarachnoid space, and the pathologic diagnosis revealed an ependymal cyst. We analyzed this case with review of other literatures.

Keyword

Ependymal cyst; Cerebellopontine angle; Syncope

MeSH Terms

Cerebellopontine Angle
Diagnosis
Humans
Subarachnoid Space
Syncope*

Figure

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  Fig. 1 A: Non-contrast computed tomography scan revealed a 6.6×5.4 cm sized large cystic lesion of the left posterior cerebellopontine angle. B and C: Magnetic resonance imaging demonstrated cystic lesion, just like an arachnoid cyst, which shift cerebellar hemisphere, pons and medulla to right side.

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  Fig. 2 A: Simple cuboidal epithelial cells of cystic lining without prominent cilia (H&E, ×400). B: Glial fibrillary acidic protein positive lining epithelium (×200). C: Dot-like positivity for epithelial membrance antigen (×400).

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