Renal Angiomyolipoma, 6 Cases

Kim, Hyeon Hoe; Choi, Hwang; Lee, Chongwook

Abstract

Renal angiomyolipoma is a rare benign tumor and often associated with tuberous sclerosis. During the last 11 years 6 patients with renal angiomyolipoma were managed at Seoul National University Hospital. One patient with known tuberous sclerosis had bilateral tumors which were multiple and massive as well as extrarenal lesions. Five other patients had unilateral tumor. Two most common presentations were flank or abdominal pain and palpable renal mass but hematuria appeared in only two patients. In four patients preoperative diagnosis were possible and two of them were managed successfully with selective renal arterial embolization. Three patients are free of disease for 3 to 6 years after nephrectomy and one patient is free of symptoms for 7 months following selective renal arterial embolization. One patient is alive with mild azotemia after nephrectomy followed by embolization. One patient died of acute fulminate hepatitis on postoperative 19th day after nephrectomy.