J Korean Soc Radiol.  2014 Jan;70(1):31-34. 10.3348/jksr.2014.70.1.31.

Unilateral Pulmonary Vein Atresia: A Case Report

• Yoon SH
• Kim KJ

• KMID: 1897257
• DOI: http://doi.org/10.3348/jksr.2014.70.1.31

Abstract

Unilateral pulmonary vein atresia is a rare congenital anomaly. Its symptoms begin to manifest in childhood and a broad spectrum of clinical severity has been described, ranging from asymptomatic, recurrent pulmonary infection, severe hemoptysis, to death. Only a few adult cases with this condition, with no or mild symptoms, have been reported. Pulmonary angiography has been typically used for definite diagnosis. However, pulmonary angiography may be replaced with the current developing multidetector CT. This report presents an adult case with mild symptoms, diagnosed by multidetector CT.

MeSH Terms

Adult
Angiography
Diagnosis
Hemoptysis
Humans
Multidetector Computed Tomography
Pulmonary Veins*

Figure

• 

  Fig. 1 Rt. pulmonary vein atresia in 16-year-old man. Chest radiograph shows a small right hemithorax and diminished vessel size in the right lung with slight mediastinal displacement to the right.

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  Fig. 2 Rt. pulmonary vein atresia in 16-year-old man. A. Axial CT scan (lung window) shows small right hemithorax with mild interlobular septal thickening in right lower lobe and right middle lobe. B. Contrast-enhanced axial CT scan (mediastinal window) shows the small right pulmonary artery and normal left pulmonary artery. C, D. Axial and coronal CT scan shows smooth margin of the left atrium with no pulmonary vein (thin arrows) and numerous dilated vessels seen on paraesophageal area, representing bronchial collaterals (thick arrow).

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  Fig. 3 Rt. pulmonary vein atresia in 16-year-old man. Volume-rendered CT angiogram shows the diminutive right pulmonary artery.

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