Korean J Urol.  2007 Jun;48(6):652-654. 10.4111/kju.2007.48.6.652.

Unilateral Renal Cystic Disease

• Park BS
• Kim TH
• Lim SJ
• Lee HL
• Jeon SH

• KMID: 1885549
• DOI: http://doi.org/10.4111/kju.2007.48.6.652

Abstract

Unilateral renal cystic disease (URCD) is a rare, non-familial, non-progressive renal disorder that is not associated with cysts or disorders in other organs, and it is not related to other genetic cystic diseases. URCD is pathologically indistinguishable from autosomal dominant polycystic kidney disease (ADPKD). However, URCD is clinically and radiologically characterized by a negative family history, normal renal function and unilateral localization. We present here a case in which the final diagnosis was made by pathologic documentation through laparoscopic radical nephrectomy. This is the 26th case that has been reported on in the medical literature, and this case was pathologically diagnosed.

Keyword

Cystic renal diseases; Laparoscopy; Nephrectomy

MeSH Terms

Diagnosis
Humans
Kidney Diseases, Cystic
Laparoscopy
Nephrectomy
Polycystic Kidney, Autosomal Dominant

Figure

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  Fig. 1 T2-weighted gadolinium-enhanced coronal (A) and axial (B) magnetic resonance imaging. The enlarged left kidney is entirely filled with multiple round, well-marginated cysts of various sizes without capsule formation. Normally enhancing renal parenchyma is noted between the cysts.

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  Fig. 2 (A) Gross specimen of the cut surface of the excised kidney showing various-sized multiple cysts with the focally remaining renal parenchyma seen as septae. (B) Histologic finding of the specimen showing multiple cysts of various sizes and focal thickening of septae containing glomeruli and tubules (H&E, ×20).

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