Korean J Thorac Cardiovasc Surg.  2005 Sep;38(9):633-636.

Modified Starnes Operation for Neonatal Stenotic Ebstein Anomaly

Affiliations
  • 1Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine. tjyun@amc.seoul.kr

Abstract

Sixteen-day-old baby with severe Ebstein anomaly underwent emergency operation to relieve progressive hypoxia and congestive heart failure. Operative findings showed huge right atrium and atrialized right ventricle (aRV) with very small functional RV by distal displacement of tricuspid valve mechanism. We elected to perform modified Starnes operation because biventricular repair was deemed unattainable. After pulmonary and tricuspid valves were primarily closed, aRV was obliterated with multiple sutures from RV apex to the base. Then a PTFE (Gore-Tex, USA) vascular graft was interposed between innominate artery and main pulmonary artery for systemic to pulmonary shunt. The patient was discharged uneventfully, and received bi-directional cavopulmonary shunt 6 months later.

Keyword

Congenital heart disease; Ebstein's anomaly; Surgery method

MeSH Terms

Anoxia
Brachiocephalic Trunk
Ebstein Anomaly*
Emergencies
Heart Atria
Heart Bypass, Right
Heart Defects, Congenital
Heart Failure
Heart Ventricles
Humans
Polytetrafluoroethylene
Pulmonary Artery
Sutures
Transplants
Tricuspid Valve
Polytetrafluoroethylene
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