Korean J Med.  2014 Jan;86(1):96-101. 10.3904/kjm.2014.86.1.96.

Malignant Perivascular Epithelioid Cell Tumor (PEComa) Arising in the Omentum with Metastatic Peritoneal Seeding: A Case Report

• Jang SB
• Suh WY
• Jeon JH
• Park KW
• Lim DH
• Namgung H
• Lee SI

• KMID: 1867325
• DOI: http://doi.org/10.3904/kjm.2014.86.1.96

Abstract

The World Health Organization (WHO) defines a perivascular epithelioid cell tumor (PEComa) as a mesenchymal neoplasia composed of perivascular epithelioid cells with characteristic morphological and immunohistochemical features. They are rarely malignant. Indeed, only a few cases have been reported in the English literature, and this is the first case of PEComa reported in Korea. A 64-year-old man presented with an abdominal mass and peritoneal seeding. The patient underwent mass excision with descending colon resection and anastomosis. The primary mass and peritoneal seeding was diagnosed as a PEComa histopathologically. Seven months later, he developed liver metastasis and aggravated peritoneal seeding. Here, we report a case of malignant PEComa of the omentum.

Keyword

Perivascular epithelioid cell neoplasms; HMB-45 protein

MeSH Terms

Colon, Descending
Epithelioid Cells*
Humans
Korea
Liver
Middle Aged
Neoplasm Metastasis
Omentum*
Perivascular Epithelioid Cell Neoplasms
World Health Organization