Korean J Gastroenterol.  2012 Feb;59(2):189-192. 10.4166/kjg.2012.59.2.189.

A Case of Isolated Hepatic Lymphangioma

• Ak SJ
• Park SK
• Park HU

• KMID: 1792826
• DOI: http://doi.org/10.4166/kjg.2012.59.2.189

Abstract

Hepatic lymphangioma is a rare benign neoplasm. It usually occurs as a part of systemic lymphangiomatosis. Isolated hepatic lymphangioma is extremely rare. A 58-year-old woman with weight loss was referred for the evaluation of chronic renal insufficiency and hepatic mass. Abdominal computed tomography showed 3 cm sized multilobulated cystic lesion with calcification and thick septal enhancing focus in the segment V of the liver. On abdominal magnetic resonance imaging, the masses exhibited low signal intensity on the T1-weighted images and high signal intensity on the T2-weighted images. Malignant tumor could not be ruled out, and therefore, the patient underwent right anterior segmentectomy of the liver. Gross pathology reveraled a 3.0x2.2x1.5 cm mass with multichamber cyst, which was filled with mucoid material. Histologically the mass was composed of irregularly shaped vascular channels filled acellular homogeneous lymph fluids. The final diagnosis was hepatic isolated cavernous lymphangioma. Herein, we report a case of isolated hepatic lymphangioma and also review the existing literature.

Keyword

Lymphangioma; Liver

MeSH Terms

Female
Humans
Liver Diseases/*diagnosis/pathology/radiography
Lymphangioma/*diagnosis/pathology/radiography
Middle Aged
Renal Insufficiency, Chronic/diagnosis
Tomography, X-Ray Computed

Figure

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  Fig. 1 Abdominal CT finding. It showed 3 cm sized multilobulated cystic lesion with calcification and thick septal enhancing focus in the S5 of the liver.

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  Fig. 2 Abdominal MRI finding. (A) The mass showed low signal intensity on the T1-weighted image and (B) high signal intensity on the T2-weighted image.

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  Fig. 3 Gross finding. The cut surface revealed a cyst with multichamber, measuring 3.0×2.2×1.5 cm in dimensions, which was filled with mucoid material.

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  Fig. 4 Microscopic finding. (A) Mass was composed of irregularly shaped vascular channels filled acellular homogeneous lymph fluids (H&E, ×40). (B) Vascular channels were lined by a single layer of cuboidal cells which reacted positively for factor VIII antigen (peroxidaseanti-peroxidase stain, ×40).

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