J Korean Med Sci.  2005 Feb;20(1):158-161. 10.3346/jkms.2005.20.1.158.

Humerus Varus in a Patient with Pseudohypoparathyroidism

• Cho TJ
• Choi IH
• Chung CY
• Yoo WJ
• Yang SW

• KMID: 1781746
• DOI: http://doi.org/10.3346/jkms.2005.20.1.158

Abstract

A 7-yr-old girl presented with progressive shortening of the right upper arm and limitation of shoulder motion. Pseudohypoparathyroidism associated with Albright's hereditary osteodystrophy was diagnosed by biochemical, hormonal and radiographic studies. Her condition was complicated by severe humerus varus on the right side. Proximal humeral valgization osteotomy and concomitant humeral lengthening resulted in an improvement of the shoulder joint motion and activity in daily life.

Keyword

Pseudohypoparathyroidism; Humerus; Bone Lengthening

MeSH Terms

Bone Diseases/*complications/*diagnosis
Bone Diseases, Developmental/diagnosis
Bone Lengthening
Child
Female
Foot/radiography
Hand/radiography
Humans
Humerus/*radiography
Joint Deformities, Acquired/diagnosis
Osteotomy
Pseudohypoparathyroidism/*complications
Time Factors

Figure

• 

  Fig. 1 Preoperative photograph and radiographs. (A) The right humerus is 5 cm shorter than the contralateral side at the age of 8 yr and 10 months. (B) Humerus varus deformity is observed on the right side. (C) All the metacarpals and phalanges are short and thick. (D) Brachymetatarsia of the 3rd, 4th and 5th resulting from premature physeal closure is observed.

• 

  Fig. 2 Photographs and radiograph at the 4 yr follow-up. (A) Radiograph of the right humerus 4 yr after the operation. (B) Residual right humeral shortening is 1.2 cm.

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