Korean J Dermatol.  1991 Apr;29(2):252-255.

A case of phakomatosis pigmentovascularis association with congenital temporal alopecia

• Choi SB
• Lee JY
• Kim YH
• Houh W

Abstract

Phakomatosis pigmentovascularis is characterized by the coexistence of pigmentary and vascular nevi, which are occasionally associated with systemic organ involvement. We report a 12-year-old male, who showed bilateral nevus of Ota on the forehead, periorbital area, sclera and soft palate, nevus of Ito on the scapular area, mongolian spot on the sacral area and widespread nevus flammeus. He was also associated with congenital temporal alopecia on the lower portion of left temporal region since birth.

Keyword

Congenital temporal alopecia; Phakomatosis pigmentovascular is

MeSH Terms

Alopecia*
Child
Forehead
Humans
Male
Mongolian Spot
Neurocutaneous Syndromes*
Nevus
Nevus of Ota
Palate, Soft
Parturition
Port-Wine Stain
Sclera