J Korean Ophthalmol Soc.  1997 Mar;38(3):413-416.

A Case of Congenital Glaucoma Associated with Phakomatosis Pigmentovascularis

Affiliations
  • 1Department of Ophthalmology, Korea University College of Medicine, Seoul, Korea.

Abstract

Phakomatosis pigmentovascularis is a developmental syndrome associated with cutaneous hemangioma with melanocytic or epidemal nevi. It was first reported in 1947 by Ota, and can be classified into localized and systemic forms. Melanosis oculi is a common finding in phakomatosis pigmentovascularis, and glaucoma has also been reported. The authors report a case of bilateral congenital glaucoma associated withphakomatosis pigmentovascularis type IIb in a 2-month-old girl who underwent trabeculotomy, followed by successful control of intraocular pressure for the period of 12 months follow-up.

Keyword

Phakomatosis pigmentovascularis, Congenital glaucoma

MeSH Terms

Female
Follow-Up Studies
Glaucoma*
Hemangioma
Humans
Infant
Intraocular Pressure
Melanosis
Neurocutaneous Syndromes*
Nevus
Trabeculectomy
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