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Korean Circ J.  2012 Dec;42(12):861-865. 10.4070/kcj.2012.42.12.861.

Two Cases of High Output Heart Failure Caused by Hereditary Hemorrhagic Telangiectasia

Affiliations
  • 1Department of Cardiology, Korea University College of Medicine, Seoul, Korea. wjshimmd@unitel.co.kr

Abstract

High-output cardiac failure is a rare complication of hereditary hemorrhagic telangiectasia (HHT) usually caused by shunting of blood through atriovenous malformations (AVMs) in the liver. We describe two cases of high output heart failure due to large hepatic AVMs. Clinical suspicion of HHT based on detailed history taking and physical examination is essential for early detection and proper management of heart failure associated with HHT.

Keyword

Heart failure; Telangiectasia, hereditary hemorrhagic

MeSH Terms

Heart
Heart Failure
Liver
Physical Examination
Telangiectasia, Hereditary Hemorrhagic
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