Brain Tumor Res Treat.  2023 Oct;11(4):271-273. 10.14791/btrt.2023.0027.

Massive Hyperostotic Meningioma En Plaque Mimicking Fibrous Dysplasia

• Park JI
• Park CK
• Park BJ
• Choi SK

• KMID: 2547416
• DOI: http://doi.org/10.14791/btrt.2023.0027

Abstract

The authors report an extremely rare case of a massive hyperostotic meningioma en plaque, which had characteristics of unique bony growth. A 34-year-old man presented with a palpable solid mass in the left cranial region that had gradually grown in size with a broad base on the calvarium for 8 years. Radiologically, the area involved by the mass ranged from the sphenoid bone to the frontal, parietal, temporal, and occipital bones. Three-dimensional CT revealed multiple growing spiculate features on the inner and outer cranial surface. Even though the radiologic features resembled fibrous dysplasia, it was histologically found to be a type of meningioma.

Keyword

Meningioma; Hyperostosis; Craniofacial fibrous dysplasia

Figure

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  Fig. 1 Imaging findings of patient. A and B: Three-dimensional CT scan with bony reconstruction showing diffuse bony hyperostosis in the outer and inner surface of the cranial vault crossing the sagittal suture. C: Coronal image of a gadolinium-enhanced gradient-echo T1-weighted MRI showing mushroom-like growth combined with tumor under the dermis (arrow).

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  Fig. 2 Light microscopic findings demonstrate nodular tumor tissues, consisting of interlacing and whirling bundles of meningothelial cells without significant atypia (H&E, ×100). H&E, hematoxylin and eosin.

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