Tuberc Respir Dis.  1982 Dec;29(4):225-230. 10.4046/trd.1982.29.4.225.

Neurofibromatosis, Massive Pleural Effusion and Buldging Mass on the Right Chest Wall

• KMID: 2528822
• DOI: http://doi.org/10.4046/trd.1982.29.4.225

Abstract

Neurofibromatosis is a rare syndrome characterized by abnormal cutaneous pigmentation and numerous skin tumors. Although the syndrome was previously described by Smith in 1849, Von Recklinghausen reported two cases of multiple skin and subcutaneous tumors in 1882 and was the first to recognize their neural origin. The protean manifestations of neurofibromatosis often not fully appreciated. Various tumors developed with this disease but sarcomatous degeneration of neurofibroma was the most common findings. We reviewed clinical findings of 18-year-old female patients who was suffered from right lateral chest pain and buldging mass on the right chest wall. Sarcomatous degeneration of neurofibromatosis was confirmed by open biopsy.