Ann Dermatol.  2018 Dec;30(6):733-735. 10.5021/ad.2018.30.6.733.

An Atypical Erythromelalgia on the Chest

• Lee SH
• Yoon HS
• Yeom SD
• Byun JW
• Choi GS
• Shin J

• KMID: 2428936
• DOI: http://doi.org/10.5021/ad.2018.30.6.733

Abstract

No abstract available.

MeSH Terms

Erythromelalgia*
Thorax*

Figure

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  Fig. 1 Recurrent large purpuric erythematous annular patch on the left side of the chest. (A) Photograph taken in May 2015. Patient had had recurrent eruptions at the same location 6, 8, and 10 years previously. (B) January 2009 photograph shows a large erythematous patch with purpuric papules on the left chest, which regressed completely without treatment. Black circles indicate the biopsy sites (A: margin of erythematous patch, B: purpuric papule). We received the patient's consent form about publishing all photographic materials.

• 

  Fig. 2 Two skin biopsies collected in January 2009 and May 2015 yielded the same results. (A, B) Biopsy was taken at the margin of the patch in May 2015: dilated capillaries in upper dermis and otherwise unremarkable findings. (C, D) Biopsy was taken at the purpuric papule in January 2009: histopathology revealed thin epidermis with flattened dermoepidermal junction and telangiectasia in dermis. H&E, (A, C) ×40 and (B, D) ×200.

Reference

1. Cohen JS. Erythromelalgia: new theories and new therapies. J Am Acad Dermatol. 2000; 43:841–847.

2. Davis MD, O'Fallon WM, Rogers RS 3rd, Rooke TW. Natural history of erythromelalgia: presentation and outcome in 168 patients. Arch Dermatol. 2000; 136:330–336.

3. Patel M, Femia AN, Eastham AB, Lin J, Canales AL, Vleugels RA. Facial erythromelalgia: a rare entity to consider in the differential diagnosis of connective tissue diseases. J Am Acad Dermatol. 2014; 71:e250–e251.

4. Mosel DD, Rosler D. Erythromelalgia presenting after neurosurgical intervention in a patient with multiple malformations of the spinal cord. J Am Acad Dermatol. 2011; 65:e120–e122.

5. Gaur S, Koroscil T. Late-onset erythromelalgia in a previously healthy young woman: a case report and review of the literature. J Med Case Rep. 2009; 3:106.