J Korean Soc Radiol.  2018 Aug;79(2):101-105. 10.3348/jksr.2018.79.2.101.

Isolated Myxoma in the External Auditory Canal: A Case Report

• Park AR
• Kim TG
• Kim HJ
• Cho WH
• Kim JH
• Jeong MJ
• Kim SH
• Kim JY
• Kim SH
• Kang MJ
• Lee JH
• Bae KE

• KMID: 2416396
• DOI: http://doi.org/10.3348/jksr.2018.79.2.101

Abstract

Myxoma is a benign mesenchymal neoplasm found in the heart, bone, and other soft tissues. However, myxoma of the external auditory canal is extremely rare. Since myxoma of the external auditory canal can be manifested as a part of the Carney complex, an autosomal dominant multiple familial neoplastic disorder, correct diagnosis and thorough investigation is important. We report a case of a 59-year-old man who presented to hospital with a complaint of growing mass within the right external auditory canal during one month. The surgical excision was done, and the histopathological examination revealed myxoma. In this article, we report the magnetic resonance imaging and computed tomography findings of the myxoma of the external auditory canal and correlate with the histopathological finding.

MeSH Terms

Carney Complex
Diagnosis
Ear Canal*
Heart
Humans
Magnetic Resonance Imaging
Middle Aged
Myxoma*
Tomography, X-Ray Computed

Figure

• 

  Fig. 1 An isolated myxoma in the external auditory canal in a 59-year-old man with a growing mass within the right external auditory canal. A. On physical examination, about 2 cm-sized dark reddish, oval-shaped mass is obstructing the right external auditory canal. B. The well-defined multilobulated mass (arrows) shows markedly high signal intensity with internal low signal intensity septae on T2-weighted image (T2WI) and intermediate to subtle low signal intensity on T1-weighted image (T1WI). On Gd-enhanced fat-suppressed coronal and axial T1WI, the mass shows strong enhancement, accompanied by internal non-enhancing area which is markedly hyperintense on T2WI and hypointense on T1WI (not shown). C. On axial CT image with bone window setting, the obstructing mass (arrows) displaces the tympanic membrane medially. The external auditory canal is not widened, and there is no definite bony erosion or destruction. On coronal CT image with soft tissue window setting, the mass shows heterogeneous density, which contains high attenuated portion of about 60 Hounsfield unit. D. Histopathologic examination shows the relatively well circumscribed mass under the skin (H&E stain, × 10). The tumor is composed of bland spindled to stellate cells and many thin-walled vessels in the myxoid stroma. No definite mitosis is identified (H&E, × 200). H&E = hematoxylin and eosin

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