Korean J Dermatol.
2016 Dec;54(10):811-813.
Late-onset Segmental Neurofibromatosis on the Face
- Affiliations
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- 1Department of Dermatology, VHS Medical Center, Seoul, Korea. zooooz@hanmail.net
Abstract
- Segmental neurofibromatosis is a rare form of neurofibromatosis that is characterized by neurofibromas and/or café au lait macules, limited to one region of the body. The neurofibromas of segmental neurofibromatosis are most commonly occupied by either a cervical or a thoracic dermatome. Segmental neurofibromatosis on the face is extremely rare, and only 10 cases have been described so far. Herein, we report a case of segmental neurofibromatosis on the V1 dermatome for its rarity and unusual location.
