J Korean Radiol Soc.
1979 Jun;15(1):124-127. 10.3348/jkrs.1979.15.1.124.
Two cases of cystic angiomatosis of skeletal system
- KMID: 2349358
- DOI: http://doi.org/10.3348/jkrs.1979.15.1.124
Abstract
- The term cystic angiomatosis of the skeletal system, was suggested by Jacobs and Kimmelstiel in 1963, to describe a condition characterized by multiple cystic lesions in the skeleton, considered by them to be due tonumerous scattered hemangiohamartomata. After then many pathologist have described that as a type of hemaniomataor lymphagiomata. Recently cystic angiomatosis of bone is only on expression of a broader disease entity, the pathologic common denominator of which is a hamartomatous cystic vascular malformation, and its incidence is muchrare. We report two cases of cystic angiomatosis of skeletal system poved radiologically. One of the cases was 22 years old house wife who has had palpable thrill on the left antecubital fossa. pain on the left forearm, exertional dyspnea, and palpitation for about several months. On the simple film of the chest and the left forearm, there was no pathologic bony change. On the brachial angiogram, multiple saccular and nodular vasculardilatations and early venous filling were noted. The other cases was 23 years old female who as had pain and superficial venous dilatation on the right forearm for about 5 years. On the simple films of the chest and theright forearm of the second case, there was mild cardiomegaly and multiple small round osteolytic bony destructions without sclerotic margins in the radius, ulna, and 3rd metacapal bone, aminly in the radialmetaphsis. Radiolucent striations mimic dilated vascular pattern were also noted in the shaft of the radius, and phalangeal bones of index, middle, and ring fingers. Cortical erosion was noted in the ulna aspect of the distalradius without periosteal reactions. On the physical examination of these, involved arms were longer than intactarms about 1.6cm or 4.0cm on each cases.
