J Pathol Transl Med.  2016 Jul;50(4):309-311. 10.4132/jptm.2015.12.03.

IgG4-Related Sclerosing Mesenteritis

• Lee SJ
• Park CK
• Yang WI
• Kim SK

• KMID: 2345555
• DOI: http://doi.org/10.4132/jptm.2015.12.03

Abstract

No abstract available.

MeSH Terms

Panniculitis, Peritoneal*

Figure

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  Fig. 1. (A) A 7.9 cm lobulated mass with multiple variable calcifications is seen in the right lower abdomen on abdominal computed tomography. (B) An ill-defined whitish fibrotic lesion is noted in the mesentery.

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  Fig. 2. (A, B) The microscopic findings show fat necrosis and a sclerosing fibrotic lesion (storiform fibrosis) with lymphocytic aggregation within the germinal center formation and spindle cell proliferation. (C) Obliterative phlebitis just next to an artery is also seen.

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  Fig. 3. (A) A low Ki-67–labeling index is shown with increase only in the lymphoid follicle. The IgG4-positive cells (C)/IgG-positive cells (B) ratio is higher than 90%.

Reference

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