J Korean Neurol Assoc.
2001 Sep;19(5):544-546.
A Case of Kennedy Syndrome Mimicking Myasthenia Gravis
- Affiliations
-
- 1Department of Neurology, Hallym University College of Medicine.
- 2Division of Genetic Disease, National Institute of Health, Korea.
- 3Department of Pediatrics, Yonsei University College of Medicine.
Abstract
- Patients with Kennedy syndrome, which progresses more slowly than amyotrophic lateral sclerosis show a mild degree of motor fluctuation but rarely show significant decremental responses to repetitive nerve stimulations. Even in a patient with decremental responses to repetitive nerve stimulations, there is usually no significant improvements in motor symptoms to anticholinesterases. We experienced a patient with Kennedy syndrome, who showed significant decremental responses to repetitive nerve stimulations and a marked degree of motor fluctuation. His motor fluctuation responded dramatically to anticholinesterase. (J Korean Neurol Assoc 19(5):544~546, 2001)
