Korean J Urol.  2011 Sep;52(9):647-649.

Anuria in a 9-Month-Old Infant Resulting from Ureteral Cystine Stones

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Abstract

Pediatric urolithiasis and calcular anuria in early infancy are rare. Cystine stones may develop in utero or during early infancy. We report the case of a female 9-month-old infant with obstructive anuria resulting from cystine stones in a single functioning unit. She presented to the emergency department owing to the absence of micturition for 3 days. Radiological investigations revealed four left ureteral stones and an atrophic right kidney resulting from a calcular obstruction. Her laboratory values were as follows: serum creatinine 6.7 mg/dl, Na 132 mEq/l, K 6 mg/dl, and hematocrit 32%. An urgent percutaneous nephrostomy tube was inserted into the left side for urinary drainage, and her serum levels of creatinine and K returned to normal within 3 days. A left ureterolithotomy was the final management. Stone analysis revealed pure cystine crystals.

Keyword

Anuria; Infant; Urolithiasis

MeSH Terms

Anuria
Creatinine
Cystine
Drainage
Emergencies
Female
Hematocrit
Humans
Infant
Kidney
Nephrostomy, Percutaneous
Ureter
Urination
Urolithiasis
Creatinine
Cystine

Figure

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  FIG. 1 (A) Preoperative ultrasonography of the left kidney showing mild hydronephrosis due to ureteral stones with good corticomedullary differentiation. (B) Preoperative renal ultrasonography showing right atrophic hyperechoic kidney with loss of corticomedullary differentiation associated with stones.

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  FIG. 2 Preoperative plain abdominal X-ray kidney, ureter, and bladder showing multiple bilateral calculi (arrows).

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