Korean J Dermatol.  2004 Aug;42(8):1045-1047.

An Unusual Case of Porokeratotic Eccrine Ostial and Dermal Duct Nevus on the knee and the perianal region

• Chin HW
• Jo JH
• Jang HS
• Oh CK
• Kwon KS

Abstract

Porokeratotic eccrine ostial and dermal duct nevus (PEODDN) is a rare, benign congenital hamartoma involving the eccrine sweat duct. Histologically, the distinctive feature of PEODDN is the existence of keratinous plugs that represent cornoid lamellae overlying dilated infundibula of eccrine ducts. Lesions are typically asymptomatic papules or plaques that are located on the distal extremities, including palms, fingers and soles. We report a case of a 7-year old girl with PEODDN who exhibited lesions on the left knee and the perianal region.

Keyword

Porokeratotic eccrine ostial and dermal duct nevus (PEODDN)

MeSH Terms

Child
Extremities
Female
Fingers
Hamartoma
Humans
Knee*
Nevus*
Sweat