Korean J Pediatr.  2004 Feb;47(2):214-216.

A Case of Systemic Sclerosis in a Child

Affiliations
  • 1Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea. sonbk@inha.ac.kr
  • 2Department of Internal Medicine, College of Medicine, Inha University, Incheon, Korea.

Abstract

Systemic sclerosis is a connective tissue disease involving primarily the skin and subcutaneous tissue but may involve other organ systems such as the lungs, gastrointestinal tract, and heart. Systemic sclerosis is a rare childhood disease. The age of onset for patients with systemic sclerosis has its peak between 30 and 50 years of age. Only 1 to 2% of all patients with systemic sclerosis have disease onset before the age of 10 years of age. We report a case of systemic sclerosis in a 7-year-old female who showed Raynaud's phenomenon as an initial manifestation.

Keyword

Raynaud's phenomenon; Systemic sclerosis

MeSH Terms

Age of Onset
Child*
Connective Tissue Diseases
Female
Gastrointestinal Tract
Heart
Humans
Lung
Scleroderma, Systemic*
Skin
Subcutaneous Tissue
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