Korean J Otolaryngol-Head Neck Surg.  2004 Mar;47(3):268-271.

Two Cases of the Landau-Kleffner Syndrome

• Woo HY
• Chung SW
• Han DH
• Cho CK

Abstract

Landau-Kleffner syndrome, or acquired epileptiform aphasia, is an epilepsy syndrome with variable disruption of acquired language and epileptiform discharges on electroencephalograph (EEG). Auditory agnosia can deteriorate into total unresponsiveness and impaired expressive communication. In spite of the presence of this condition, the pure tone audiometry, otoacoustic emission and brainstem evoked auditory potential could be normal. Therefore, in the above hearing tests which are the mainstream methods for pediatric hearing evaluation, otolaryngologists should have suspicion for the presence of this syndrome, although it is rare.

Keyword

Landau-Kleffner syndrome; Auditory agnosia; Epilepsy

MeSH Terms

Agnosia
Audiometry
Brain Stem
Epilepsy
Hearing
Hearing Tests
Landau-Kleffner Syndrome*