Korean J Med.
2013 May;84(5):698-703.
A Case of Peutz-Jeghers Syndrome with Small Bowel Neuroendocrine Carcinoma
- Affiliations
-
- 1Department of Gastroenterology, Internal Medicine, Dong-A University College of Medicine, Busan, Korea. jsjang@dau.ac.kr
- 2Department of Radiology, Dong-A University College of Medicine, Busan, Korea.
- 3Department of Pathology, Dong-A University College of Medicine, Busan, Korea.
Abstract
- Peutz-Jeghers syndrome (PJS) is an autosomal dominant inherited disorder characterized by hamartomatous polyps in the gastrointestinal tract and mucocutaneous melanin pigmentation. Hamartomas are not generally regarded as premalignant, although patients with PJS are at increased risk for common and unusual types of gastrointestinal and non-gastrointestinal malignancies. However, most of the reported gastrointestinal malignancies have been adenocarcinomas, and few reports of an association of this syndrome with a neuroendocrine tumor (NET) have been published. Moreover, no case of this syndrome with NET has been reported in Korea. Here, we report a 21-year old male with PJS who had a small bowel neuroendocrine carcinoma.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Peutz-Jeghers syndrome: a new understanding
- A Case of Peutz-Jegher's Syndrome
- A Case of Peutz-Jeghers Syndrome with Small Bowel Perforation and Enteritis Cystica Profunda
- CT Enteroclysis and Intraoperative Endoscopic Polypectomy for Peutz-Jeghers Syndrome with Advanced Rectal Carcinoma: A Case Report
- Intraoperative Enteroscopic Total Polypectomy for the Patients with Peutz-Jeghers Syndrome
