J Korean Ophthalmol Soc.
1976 Dec;17(4):545-549.
A Case Report of Madan's Syndrome
- Affiliations
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- 1Department of Ophthalmology, St. Mary's Hospital, Catholic Medical Collge, Seoul, Korea.
Abstract
- Marfan's Syndrome was a collagenous hereditary disorder affected by the long bone, heart and eyes. This typical arachnodactyly patient was 8 year old boy who has had visual disturbance due to central opacitous lens subluxation of both eyes. We performed successfull intracapsular lens extraction by use of cryolens extractor for both eyes. X-ray chest suggested the evidence of aortic aneurysm. Electron microscopic study for the zonular fibers of the lens showed a relative loose aggregated zonular fibers with small amount of its bundles, but chromosomal study for this patient showed no abnormality.
