J Korean Pediatr Cardiol Soc.  2004 Jun;8(1):181-186.

A Case of Hypertrophic Cardiomyopathy Associated with Wolff-Parkinson-White Syndrome

Affiliations
  • 1Department of Pediatrics, College of Medicine, The Catholic University of Korea, Seoul, Korea.

Abstract

Hypertrophic cardiomyopathy(HCM) is defined as a thickened wall of heart muscles and non-dilated left ventricle, but is not accompanied underlying cardiac or systemic diseases that induce ventricular hypertrophy. HCM is responsible to exercise limitation for all ages and also is known as the most common cause of heart-related sudden death during childhood and adolescents. Epidemiological studies showed that prevalence in young adults is 0.2% and HCM is caused by a mutations in genes that code the proteins of cardiac muscles. HCM with Wolff-Parkinson-White Syndrome is extremely rare and associated with a high risk of tachyarrhythmia and sudden death. We report an infantile HCM with WPW syndrome who died suddenly.

Keyword

Wolff-Parkinson-White Syndrome; Hypertrophic cardiomyopathy; Sudden cardiac death; Hydrocephalus

MeSH Terms

Adolescent
Cardiomyopathy, Hypertrophic*
Death, Sudden
Death, Sudden, Cardiac
Heart Ventricles
Humans
Hydrocephalus
Hypertrophy
Myocardium
Prevalence
Tachycardia
Wolff-Parkinson-White Syndrome*
Young Adult
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