J Korean Neurosurg Soc.
1980 Sep;9(2):505-510.
Letterer-Siwe Syndrome Associated with Multiple Skull Defects and Huge Epidural Mass: Case Report
- Affiliations
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- 1Department of Neurosurgery, Department of Pediatrics, Presbyterian Medical Center, Jeonju, Korea.
Abstract
- The authors are reporting a case of Letterer-Siwe syndrome of 24 months old female as a from of multivisceral and polyostotic involvement that was associated with multiple skull defects and huge epidural mass. The syndrome was diagnosed at the age of 8 months, and clinical improvement was achieved for more than 16 months by means of chemotherapy and surgical removal of scalp mass.
