Arch Craniofac Surg.  2016 Mar;17(1):31-34. 10.7181/acfs.2016.17.1.31.

Cutaneous Rosai-Dorfman Disease Confused with Vascular Mass

Affiliations
  • 1Department of Plastic and Reconstructive Surgery, Hallym University Sacred Heart Hospital, Hallym University Medical Center, Anyang, Korea. hallymjsw@gmail.com

Abstract

Rosai-Dorfman disease is a rare histiocytic disorder, clinically characterized by massive, bilateral painless cervical lymphadenopathy with potential for extranodal manifestations. We report a 45-year-old male patient who presented with a slowly growing erythematous nodule of the left chin. The mass appeared non-vascular on computed tomography study, but ultrasonogram was suggestive of a vascular lesion. The lesion was excised with presumptive diagnosis of a hemangioma. However, histopathologic examination of the surgical biopsy revealed histiocytic infiltration with emperipolesis, which was pathognomic for Rosai-Dorfman disease. Additional imaging studies did not reveal lymph node enlargement or other extranodal manifestation. The patient was diagnosed with cutaneous form of the Rosai-Dorfman disease and was discharged home. He remains free of local recurrence at 8 months.

Keyword

Rosai-Dorfman disease; Hemangioma; Computed tomography; Ultrasonography

MeSH Terms

Biopsy
Chin
Diagnosis
Emperipolesis
Hemangioma
Histiocytosis, Sinus*
Humans
Lymph Nodes
Lymphatic Diseases
Male
Middle Aged
Recurrence
Ultrasonography
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