Ann Dermatol.  2008 Mar;20(1):45-48. 10.5021/ad.2008.20.1.45.

A Case of Clear Cell Sarcoma Occurring on the Abdomen

• Jung SJ
• Seung NR
• Park EJ
• Kim CW
• Kim KH
• Kim KJ

• KMID: 2156361
• DOI: http://doi.org/10.5021/ad.2008.20.1.45

Abstract

Clear cell sarcoma is a rare malignant tumor representing about 1% of soft tissue tumors. It usually presents in the distal extremities of young adults, frequently attached to tendons or aponeuroses. This slowly progressive tumor tends to recur and results in eventual development of metastatic growth. Early recognition of the disease and prompt wide excision of tumor are essential to get a favorable outcome. We report a rare case of clear cell sarcoma in a 57 year-old female who presented with an erythematous hard nodule on her abdomen.

Keyword

Clear cell sarcoma

MeSH Terms

Abdomen
Extremities
Female
Humans
Sarcoma, Clear Cell
Tendons
Young Adult

Figure

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  Fig. 1 (A, B) Solitary pea sized glistening erythematous nodule with peripheral brownish patch on her right lower abdomen.

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  Fig. 2 Tumor cells are observed to be infiltrated in the dermis (A: H&E, × 40), and composed compact nests and fascicles (B: H&E, × 100). Tumor cells consist of round to ovoid vesicular nuclei and pale-staining cytoplasm (C: H&E, × 400).

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  Fig. 3 The tumor cells show reactivity with (A) S-100 protein, (B) Vimentin (Immunohistochemical stain, × 100).

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