J Cardiovasc Ultrasound.  2010 Jun;18(2):62-65. 10.4250/jcu.2010.18.2.62.

A Case of Right Ventricular Dysfunction Caused by Pectus Excavatum

• Park SY
• Park TH
• Kim JH
• Baek HK
• Seo JM
• Kim WJ
• Nam YH
• Cha KS
• Kim MH
• Kim YD

• KMID: 2135441
• DOI: http://doi.org/10.4250/jcu.2010.18.2.62

Abstract

Pectus excavatum compresses the underlying right side of the heart, which might lead to right ventricular dysfunction as illustrated in this case report.

Keyword

Right ventricular dysfunction; Pectus excavatum

MeSH Terms

Funnel Chest
Heart
Ventricular Dysfunction, Right

Figure

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  Fig. 1 On physical examination, depression of chest wall is apparent.

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  Fig. 2 Chest X-ray shows severe cardiomegaly, prominently of the right and left atria.

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  Fig. 3 Transthoracic echocardiography. Apical 4-chamber view in diastole (A) and systole (B) demonstrates reduced a fractional shortening area of right ventricular (RV). Modified 4-chamber view in diastole (C) and systole (D) shows an aneurysm-shaped RV apex which was akinetic (arrows).

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  Fig. 4 The peak velocity of the tricuspid regurgitant jet is measured at 2.4 m/s (A) and tissue Doppler systolic velocity at the tricuspid annulus was 8.0 cm/s (B). Arrow indicates peak systolic velocity.

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  Fig. 5 Measurement of the Haller index. On chest computed tomography, Haller index is calculated by dividing the inner width of the chest at the widest point (A) by the distance between the posterior surface of the sternum and the anterior surface of the spine (B). Haller index of the patient is 4.2.

Reference

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