J Cardiovasc Ultrasound.  2013 Dec;21(4):197-199. 10.4250/jcu.2013.21.4.197.

The Case of Isolated Double Atrial Septum with Persistent Interatrial Space

• Kim IS
• Jin MN
• Song C
• Kim YJ
• Ji AY
• Son JW
• Chang HJ
• Hong GR
• Ha JW
• Chung N

• KMID: 2135421
• DOI: http://doi.org/10.4250/jcu.2013.21.4.197

Abstract

Double atrial septum is very rare atrial septal malformation which has double layered atrial septum with persistent interatrial space between the two atria. Clinically, most cases of this anomaly are asymptomatic unless manifest as thromboembolic complications, such as stroke, or transient ischemic attack, that thrombus may be originated from this interatrial space. We report a case of a 69-year-old man who was diagnosed with isolated double atrial septum by transthoracic echocardiography.

Keyword

Double atrial septum; Interatrial space

MeSH Terms

Aged
Atrial Septum*
Echocardiography
Humans
Ischemic Attack, Transient
Stroke
Thrombosis

Figure

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  Fig. 1 A: Apical 4 chamber view shows slightly enlarged LA chamber, fibrothickened mitral valve with aneurismal change of interatrial septum (arrow). B: Subcostal view shows interatrial space (*) distinguished by double-layered atrial septal structure. LA: left atrium, LV: left ventricle, RA: right atrium, RV: right ventricle, MV: mitral valve.

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  Fig. 2 A: Zoomed up view of subcostal view; interatrial space (*) distinguished by double-layered atrial septal structure. B: Color Doppler shows communicating flow (arrow) between left atrium and interatrial space (*). Small patent foramen ovale with left-to-right shunt flow (arrowhead) is also shown. LA: left atrium, LV: left ventricle, RA: right atrium, RV: right ventricle.

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  Fig. 3 Axial view of computed tomography shows double atrial septum with persistent interatrial space (*). LA: left atrium, LV: left ventricle, RA: right atrium.

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