J Cardiovasc Ultrasound.  2015 Mar;23(1):54-55. 10.4250/jcu.2015.23.1.54.

Shone Complex

• Chandra S
• Kharwar RB
• Mundhekar

• KMID: 2135410
• DOI: http://doi.org/10.4250/jcu.2015.23.1.54

Abstract

No abstract available.

Figure

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  Fig. 1 Two dimensional echocardiography with color Doppler. Parasternal long axis view (A) showing the sub aortic membrane (open arrow), partial supra mitral ring attached near the posterior mitral annulus (white solid arrow) and abnormal anterior and posterior mitral leaflets. Diastolic frame in apical four chamber view showing severe degree of mitral stenosis with color flow turbulence starting at the supra mitral ring level (B). Systolic frame in apical four chamber view showing severe eccentric mitral regurgitation (C). The basal short axis view showing the quadricuspid nature of the aortic valve (D). Ao: aorta, LA: left atria, LV: left ventricle, RV: right ventricle.

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  Fig. 2 Three dimensional transthoracic echocardiography with color Doppler. The unifocal attachment of the parachute mitral valve can be clearly delineated in apical two chamber orientation (arrow in A). The sub valvular mitral stenosis was in fact caused by a slit like opening (arrowhead in B) in the parachute mitral valve. Parasternal long axis image in a systolic frame (C) clearly showing the sub aortic membrane (arrow in C). Three dimensional echocardiography clearly showing the anatomy of the sub aortic membrane (arrow in D) with a near circular membrane morphology and a central opening as viewed from the LV side. Ao: aorta, LA: left atria, LV: left ventricle.

Reference

1. Shone JD, Sellers RD, Anderson RC, Adams P Jr, Lillehei CW, Edwards JE. The developmental complex of "parachute mitral valve," supravalvular ring of left atrium, subaortic stenosis, and coarctation of aorta. Am J Cardiol. 1963; 11:714–725.

2. Brauner RA, Laks H, Drinkwater DC Jr, Scholl F, McCaffery S. Multiple left heart obstructions (Shone's anomaly) with mitral valve involvement: long-term surgical outcome. Ann Thorac Surg. 1997; 64:721–729.