J Korean Radiol Soc.  1995 Apr;32(4):639-642.

Embryonal Rhabdomyosarcoma of the Biliary Tree: A Case Report

• Lee KN
• Chung DH
• Nam KJ
• Oh JY
• Park BH
• Choi JC

Abstract

Rhabdomyosarcoma are reportedly the most common soft tissue sarcoma occuring in childhood, but the biliary tree is a rare site of origin for this tumor. Recently we experienced a case of embryonal rhabdomyosarcoma of the biliary tree in a 30-month-old child. UItrasonography showed hypoechoic mass filling the dilated left. intrahepatic & extrahepatic bile ducts, and CT showed hypodense mass with heterogeneous enhancement after contrast infusion. Intraoperative cholangiography showed filling defects within the dilated left. intrahepatic & extrahepatic bile ducts. Postoperative MRI showed residual mass within the left. intrahepatic duct which was hypointense on T1WI and hyperintense on T2WI.

MeSH Terms

Bile Ducts, Extrahepatic
Biliary Tract*
Child
Child, Preschool
Cholangiography
Humans
Magnetic Resonance Imaging
Rhabdomyosarcoma
Rhabdomyosarcoma, Embryonal*
Sarcoma