J Korean Radiol Soc.  2002 Oct;47(4):361-364. 10.3348/jkrs.2002.47.4.361.

Pleuropulmonary Blastoma: A Case Report

• Jin GY
• Han YM
• Park HH
• Chung GH
• Kim CS

• KMID: 2103658
• DOI: http://doi.org/10.3348/jkrs.2002.47.4.361

Abstract

Primary pulmonary neoplasms are uncommon in children. One such tumor, pleuropulmonary blastoma (PPB), is very rare, highly aggressive and malignant, and originates from either the lungs or pleura. It contains both mesenchymal and benign epithelial elements that resemble fetal lung, and occurs mainly in children aged less than five. The clinal symptoms often suggest upper respiratory tract infection or pneumothorax, but ultrasonography and chest CT scans depict both a large mass occupying an almost entire hemithorax, and a simple lung cyst. Contrast-enhanced CT demonstrates hetergeneous attenuation and a whorled appearance.

Keyword

Lung neoplasms, CT; Neoplasms, in infants and children

MeSH Terms

Child
Humans
Lung
Lung Neoplasms
Pleura
Pneumothorax
Respiratory Tract Infections
Tomography, X-Ray Computed
Ultrasonography