Korean J Dermatol.  2007 Jul;45(7):702-705.

A Case of Sebaceous Carcinoma on the Extraocular Area Associated withB-cell Lymphoma, Esophageal Cancer and Gastric Cancer -A Case of Muir-Torre Syndrome-

• Lee JH
• Yun SJ
• Kim SJ
• Lee SC
• Won YH
• Lee JB

Abstract

Muir-Torre syndrome (MTS) is a rare autosomal dominant genodermatoses, first described in 1967. It is characterized by the presence of sebaceous tumors and an internal malignancy in the absence of other predisposing factors. The most common internal malignancy associated with MTS is colorectal adenocarcinoma, although a wide tumor spectrum exists including carcinomas of the genitourinary tract, breast, and hematologic malignancy. It is rare for more than two internal malignancies to occur in MTS. We report a rare case of MTS with B-cell lymphoma, esophageal cancer and gastric malignancy in a 63-year-old male.

Keyword

B-cell lymphoma; Esophageal carcinoma; Gastric malignancy; Muir-Torre syndrome; Sebaceous carcinoma

MeSH Terms

Adenocarcinoma
Breast
Causality
Esophageal Neoplasms*
Hematologic Neoplasms
Humans
Lymphoma*
Lymphoma, B-Cell
Male
Middle Aged
Muir-Torre Syndrome
Stomach Neoplasms*