Korean J Urol.  2007 May;48(5):558-560. 10.4111/kju.2007.48.5.558.

Adult's Wilms' Tumor Mimicking Renal Pelvis Tumor

• Yang SO
• Joung JY
• Han KS
• Jeong IG
• Kwon KS
• Seo HK
• Chung J
• Park WS
• Lee KH

• KMID: 2061265
• DOI: http://doi.org/10.4111/kju.2007.48.5.558

Abstract

Wilms' tumor is a rare malignant renal tumor in adults and it usually presents as a parenchymal mass that resembles renal cell carcinoma. The authors observed one case of adults Wilms' tumor developing in the renal pelvis and the initial diagnosis was renal pelvis tumor. The patient underwent radical nephroureterectomy with bladder cuff excision and adjuvant chemotherapy with the combination of vincristine and actinomycin. The patient has remained healthy and was without evidence of tumor recurrence on a follow-up CT scan at 18 months postoperatively.

Keyword

Wilms' tumor; Adult; Kidney pelvis

MeSH Terms

Adult
Carcinoma, Renal Cell
Chemotherapy, Adjuvant
Dactinomycin
Diagnosis
Follow-Up Studies
Humans
Kidney Pelvis*
Recurrence
Tomography, X-Ray Computed
Urinary Bladder
Vincristine
Wilms Tumor*
Dactinomycin
Vincristine

Figure

• 

  Fig. 1 The computed tomography (CT) scan revealed a 6cm sized solid mass that was located at the pelvis of the right kidney. (A) Pre-contrast CT scan, (B) post-contrast CT scan.

• 

  Fig. 2 Grossly, a well-demarcated mass (6.0×6.0×0.5cm) was found in the renal pelvis with a grayish white, lobulated, cut surface.

• 

  Fig. 3 Microscopic histologic examination revealed that the tumor was composed of 90% undifferentiated blastemal cells (inset ×400) and 10% focal stromal components (H&E, original magnification ×100).

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