Korean J Radiol.  2007 Oct;8(5):438-442. 10.3348/kjr.2007.8.5.438.

Mazabraud's Syndrome Coexisting with a Uterine Tumor Resembling an Ovarian Sex Cord Tumor (UTROSCT): a Case Report

• Calisir C
• Inan U
• Yavas US
• Isiksoy S
• Kaya T

• KMID: 1734293
• DOI: http://doi.org/10.3348/kjr.2007.8.5.438

Abstract

The association of intramuscular myxoma and fibrous dysplasia is a rare disease known as Mazabraud's syndrome. We present a case of Mazabraud's syndrome coexisting with a uterine tumor and resembling an ovarian sex cord tumor (UTROSCT). This uterine tumor showed a high mitotic index and cytological atypia. To the best of our knowledge, the coexistence of the two different entities has not been reported in the literature.

Keyword

Fibrous dysplasia; Monostotic; Myxoma; Uterine neoplasms

MeSH Terms

Aged
Biopsy
Buttocks/pathology/surgery/ultrasonography
Diagnosis, Differential
Female
Fibrous Dysplasia, Monostotic/complications/*diagnosis/surgery
Humans
Magnetic Resonance Imaging
Myxoma/complications/*diagnosis/surgery
Ovarian Neoplasms/*diagnosis
Rare Diseases
Sex Cord-Gonadal Stromal Tumors/*diagnosis
Syndrome
Uterine Neoplasms/complications/*diagnosis/surgery