Korean J Radiol.  2014 Feb;15(1):54-60. 10.3348/kjr.2014.15.1.54.

Monosegmental Hepatobiliary Fibropolycystic Disease Mimicking a Mass: Report of Three Cases

• Kwon JH
• Kim MJ
• Kim YH
• Kang KJ
• Kang YN
• Kwon SY

• KMID: 1711477
• DOI: http://doi.org/10.3348/kjr.2014.15.1.54

Abstract

Hepatobiliary fibropolycystic diseases are a unique group of entities involving the liver and biliary tract, which are caused by abnormal embryologic development of the ductal plates at various stages. We experienced strange hepatobiliary fibropolycystic diseases with a complex mass composed of malformed ducts and biliary cysts, which did not belong to, and were different from, previously known malformations. They were unique in imaging and histologic features. We herein report three cases of monosegmental hepatobiliary fibropolycystic disease mimicking a mass.

Keyword

Ductal plate malformations; Fibropolycystic disease; Monosegmental disease; Caroli disease

MeSH Terms

Adult
Bile Duct Diseases/*diagnosis
Cysts/*diagnosis
Diagnostic Imaging/methods
Female
Fibrosis/diagnosis
Gallbladder Diseases/diagnosis
Humans
Liver Cirrhosis/diagnosis
Liver Diseases/*diagnosis
Liver Neoplasms/diagnosis
Male