Korean J Obstet Gynecol.  2009 Mar;52(3):377-381.

A case of peritoneal desmoplastic small round cell tumor

• Yang KY
• Kim YS
• Han JH
• Park YK
• Jung MH

Abstract

Desmoplastic small round cell tumor is a rare and aggressive tumor that affects young males. It is usually an abdominopelvic malignancy that demonstrates distinct histological appearances and a unique cytogenetic profile. There have been many different approaches to the treatment of desmoplastic small round cell tumor, but unfortunately it remains incurable and has poor long-term survival rates. However, with an aggressive approach to the treatment using multiple modalities, some temporary benefit to survival can be achieved. There has not yet been a case in which treatment has led to a curative outcome. Recently, we also experienced a case of very poor outcome of 31-year-old female with small round cell tumor in peritoneum. Here, we report the case with a brief review of literatures.

Keyword

Desmoplastic small round cell tumor; Peritoneum

MeSH Terms

Adult
Cytogenetics
Desmoplastic Small Round Cell Tumor
Female
Humans
Male
Peritoneum
Survival Rate