Korean J Hepatobiliary Pancreat Surg.  2013 Aug;17(3):131-134. 10.14701/kjhbps.2013.17.3.131.

Peribiliary cysts developed in normal underlying liver: report of a case

• Kim HJ
• Kim CY
• Hur YH
• Kim JC
• Cho CK
• Kim HJ

• KMID: 1472529
• DOI: http://doi.org/10.14701/kjhbps.2013.17.3.131

Abstract

Peribiliary cysts, known as cystic dilatation, of the extramural peribiliary glands of the bile duct are rare, and are usually detectable under conditions of pre-existing hepatobiliary diseases such as liver cirrhosis. Preoperative diagnosis is often difficult, because they are usually asymptomatic. Distinction of peribiliary cysts from premalignant or malignant cystic lesions is mandatory. Herein, we report a case of peribiliary cyst, which was preoperatively assumed as unilobar Caroli's diseases in healthy young patients and briefly discuss the management of the condition.

Keyword

Cyst; Hepatic neoplasm; Caroli disease

MeSH Terms

Bile Ducts
Caroli Disease
Dilatation
Humans
Liver Cirrhosis
Liver Neoplasms

Figure

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  Fig. 1 Ultrasonogram demonstrating a multiseptated cystic mass at the segment VI.

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  Fig. 2 Computed tomography scan showing a multiseptated non-enhancing cystic mass at the segment VI.

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  Fig. 3 Magnetic resonance cholangiopancreatography demonstrating a cluster of hyperintense cystic lesions on T2-weighted image involving the segment VI.

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  Fig. 4 Gross finding of peribiliary cysts. Multiple cysts distributed along the major segmental portal tract of the segment VI.

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  Fig. 5 Microphotographs of peribiliary cysts. (A) Normal appearing bile ducts are seen without inflammation and hyperplasia. (B) The peribiliary cyst is lined by flattened epithelium.

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