Korean Circ J.  2010 Sep;40(9):465-467. 10.4070/kcj.2010.40.9.465.

An Extremely Rare Variety of Anomalous Coronary Artery: Right Coronary Artery Originating From the Distal Left Circumflex Artery

• Chung SK
• Lee SJ
• Park SH
• Lee SW
• Shin WY
• Jin DK

• KMID: 1456140
• DOI: http://doi.org/10.4070/kcj.2010.40.9.465

Abstract

A single coronary artery (SCA) is a rare congenital anomaly of the coronary circulation, which is often associated with myocardial ischemia and other congenital cardiac anomalies. A 77-year-old woman visited our hospital complaining of typical chest pain. Coronary angiography revealed an isolated SCA. The right coronary artery did not originate from the aorta, but instead emerged from the distal left circumflex artery, with significant stenosis at the proximal portion of the left anterior descending artery. A stent was successfully implanted at the culprit lesion. There was no perfusion defect detected by a cardiac SPECT study.

Keyword

Coronary vessel anomalies; Angina pectoris

MeSH Terms

Aged
Angina Pectoris
Aorta
Arteries
Chest Pain
Constriction, Pathologic
Coronary Angiography
Coronary Circulation
Coronary Vessel Anomalies
Coronary Vessels
Female
Humans
Myocardial Ischemia
Perfusion
Stents
Tomography, Emission-Computed, Single-Photon

Figure

• 

  Fig. 1 Coronary angiography showed 90% stenosis at the proximal portion of the left anterior descending artery.

• 

  Fig. 2 Coronary angiography. An aberrant branch, extending from the distal left circumflex artery, continued to the right atrioventricular groove, covering the territory of the right coronary artery (A). Aortography showed the absence of the right coronary ostium (B).

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  Fig. 3 Contrast-enhanced 64-slice multi-detector cardiac computed tomography. It showed that the right coronary artery was absent (A) and the extended left circumflex coronary artery supplied the territory of the right coronary artery (B).

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