Korean Circ J.  2012 Jun;42(6):437-440. 10.4070/kcj.2012.42.6.437.

Newly Developed Aortic Dissection After Aorta Cannulation During Mitral Valve Surgery in a Patient With Marfan Syndrome

Affiliations
  • 1Division of Cardiology, Department of Internal Medicine, Gil Hospital, Gachon University of Medicine and Science, Incheon, Korea. miseung@gmail.com
  • 2Department of Thoracic and Cardiovascular Surgery, Gil Hospital, Gachon University of Medicine and Science, Incheon, Korea.

Abstract

We report a case of newly developed aortic dissection after aorta cannulation during mitral valve surgery in a patient with Marfan syndrome. An unexpected fatal complication of cardiac surgery detected on postoperative imaging survey in Marfan syndrome patient and its surgical finding are described.

Keyword

Marfan syndrome; Complications; Echocardiography; Operations

MeSH Terms

Aorta
Catheterization
Echocardiography
Humans
Marfan Syndrome
Mitral Valve
Thoracic Surgery

Figure

  • Fig. 1 Marfanoid feature of the patient (A, B and C). Mitral valve prolapse (arrow, D) and anteriorly directed severe eccentric mitral regurgitation (E) on pre-operative transesophageal echocardiography.

  • Fig. 2 There was no evidence of aortic dissection on pre-operative echocardiography (A) and newly developed dissecting flap on echocardiography performed after surgery (arrow, B). There was also no evidence of significant aortic disease on pre-operative computed tomography (C) and newly developed aortic dissection (Stanford type A) after the operation (arrows, D).

  • Fig. 3 Dissecting flap and entry site of aortic dissection at previous cannulation site at the ascending aorta (arrow, A), which was treated using the Bentall procedure (B).


Reference

1. Dietz H, Francke U, Furthmayr H, et al. The question of heterogeneity in Marfan syndrome. Nat Genet. 1995. 9:228–231.
2. Faivre L, Collod-Beroud G, Loeys BL, et al. Effect of mutation type and location on clinical outcome in 1,013 probands with Marfan syndrome or related phenotypes and FBN1 mutations: an international study. Am J Hum Genet. 2007. 81:454–466.
3. Marsalese DL, Moodie DS, Lytle BW, et al. Cystic medial necrosis of the aorta in patients without Marfan's syndrome: surgical outcome and long-term follow-up. J Am Coll Cardiol. 1990. 16:68–73.
4. Marsalese DL, Moodie DS, Vacante M, et al. Marfan's syndrome: natural history and long-term follow-up of cardiovascular involvement. J Am Coll Cardiol. 1989. 14:422–428.
5. Akhyari P, Kamiya H, Heye T, Lichtenberg A, Karck M. Aortic dissection type A after supra-aortic debranching and implantation of an endovascular stent-graft for type B dissection: a word of caution. J Thorac Cardiovasc Surg. 2009. 137:1290–1292.
6. Kumar K, Menkis AH, Jassal DS, Arora RC. Iatrogenic acute aortic dissection in a patient with Marfan syndrome: unusual site of intimal tear. Interact Cardiovasc Thorac Surg. 2009. 8:362–363.
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