Korean J Radiol.  2011 Jun;12(3):382-385. 10.3348/kjr.2011.12.3.382.

Primary Hepatic Amyloidosis: Report of an Unusual Case Presenting as a Mass

• Son RC
• Chang JC
• Choi JH

• KMID: 1122336
• DOI: http://doi.org/10.3348/kjr.2011.12.3.382

Abstract

Hepatic involvement of amyloidosis is common. Diffuse infiltration with hepatomegaly is a usual radiologic finding of hepatic amyloidosis. To our knowledge, this is the first case of amyloidosis involving the liver that presented as a mass.

Keyword

Amyloidosis; Computed tomography (CT)

MeSH Terms

Aged
Amyloidosis/*radiography/ultrasonography
Biopsy, Needle
Contrast Media/diagnostic use
Female
Humans
Liver Diseases/*radiography/ultrasonography
*Tomography, X-Ray Computed

Figure

• 

  Fig. 1 73-year-old woman with hepatic amyloidosis. A. Unenhanced CT shows high density lobulating mass with central calcification (arrow) in segment 3 of liver. B-D. Mass shows very poor delayed contrast enhancement on arterial (B), portal venous (C) and delayed (D) phase image. E. US image during needle biopsy indicates mild heterogeneous echoic mass on segment 3 of liver (arrows). F, G. Microscopically, diffuse amyloid deposits are present without viable hepatocyte (F, Hematoxylin & Eosin staining, original magnification × 200), and Congo red stain is positive (G).

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