J Korean Dysphagia Soc.  2012 Jul;2(2):62-66.

Effect of the Dysphagia Therapy Child with Nemaline Myopathy Who Have Dysphagia: A Single Subject Research Design

• Shin HJ
• Lee JS
• Lee GB

Abstract

Objective
The purpose of this study was to notify the Nemaline myopathy and to demonstrate the effect of the dysphagia therapy on this disease. Method: This study used to considered the literatures of the Nemaline myopathy and offer a dysphagia therapy since October 2007 until June 2009 on a child who has a Nemaline myopathy and evaluates her oral-motor function and changes her feeding method. Result: Direct oral sensorimotor treatment and neuromuscular electrical stimulation showed improving in a jaw and tongue movement and there again decreasing in drooling and aspiration enables non-oral feeding to partial oral feeding.
Conclusion
Continous oral sensorimotor treatment is important to patients who have a Nemaline myopathy. And neuromuscular electrical stimulation is a help to them. Needs ask to occupational therapist early on and have a multidisciplinary team approach.

Keyword

Nemaline myopathy; Dysphagia therapy; Sensorimotor treatment; Neuromuscular electrical stimulation