Korean J Med.  2020 Feb;95(1):56-60. 10.3904/kjm.2020.95.1.56.

Paroxysmal Nocturnal Hemoglobinuria Presenting with Chronic Abdominal Pain and Iron Deficiency Anemia

Affiliations
  • 1Department of Internal Medicine, Jeonggwan Ilsin Christian Hospital, Busan, Korea
  • 2Division of Gastroenterology, Department of Internal Medicine, Pusan National University Yangsan Hospital, Pusan National University College of Medicine, Yangsan, Korea
  • 3Department of Internal Medicine, Daegu Catholic University Chilgok Catholic Hospital, Daegu, Korea
  • 4Baekyang Jeil Medical Clinic, Busan, Korea

Abstract

Paroxysmal nocturnal hemoglobinuria (PNH) is a rare acquired disorder of hematopoietic stem cells characterized by chronic intravascular hemolysis, nocturnal hemoglobinuria, thromboembolic events and secondary bone marrow failure caused by uncontrolled complement activation. Generally, chronic abdominal pain and iron deficiency anemia are considered typical symptoms of gastrointestinal diseases, but are also common in PNH. We report a case of PNH presenting with chronic abdominal pain and iron deficiency anemia, along with a relevant literature review.

Keyword

발작성 야간혈색소뇨증; 만성 복통; 철결핍빈혈; Hemoglobinuria, Paroxysmal; Abdominal pain; Anemia, Iron-deficiency
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