Brain Tumor Res Treat.  2019 Oct;7(2):147-150. 10.14791/btrt.2019.7.e40.

A Case of Sporadic Suprasellar Hemangioblastoma Mimicking Meningioma

• Kang BM
• Youn SM

• KMID: 2461189
• DOI: http://doi.org/10.14791/btrt.2019.7.e40

Abstract

Hemangioblastoma (HBL) in the suprasellar region is very rare and a few cases have been reported. Suprasellar HBL without von Hippel-Lindau disease is much rarer. A 76-year old male patient presented progressively deteriorating visual disturbance. MRI demonstrated solid suprasellar mass of 20 mm in diameter, broadly based to planum sphenoidale and diaphragm sella and dural tail sign after the administration of gadolinium diethylene triamine penta-acetic acid (Gd-DTPA). Preoperative diagnosis was meningioma. Total resection of the tumor was not accomplished because of massive hemorrhage, and the histopathologic examination revealed the tumor to be HBL. The visual disturbance of the patient was not improved. The authors reviewed the literature and considered a differential diagnosis of suprasellar tumors and treatment of suprasellar HBL.

Keyword

Hemangioblastoma; Suprasellar; von Hippel Lindau disease

MeSH Terms

Diagnosis
Diagnosis, Differential
Diaphragm
Gadolinium
Hemangioblastoma*
Hemorrhage
Humans
Magnetic Resonance Imaging
Male
Meningioma*
Tail
Temazepam
von Hippel-Lindau Disease
Gadolinium
Temazepam

Figure

• 

  Fig. 1 Preoperative axial MRI without contrast enhancement showing isointense on T1-weighted image and hyperintense on T2-weighted image suprasellar mass of 20 mm in diameter (A and B). Sagittal and coronal image with contrast enhancement demonstrated homogeneously enhancing solid mass broadly based to planum sphenoidale and diaphragm sella and strong dural tail sign (arrow) (C and D).

• 

  Fig. 2 Hematoxylin and eosin staining showing two different components characterized by numerous thin walled capillary vessels and stromal cells, which are characteristically clear and vacuolated cytoplasm were seen in low and high magnification [×200 (A), ×400 (B)]. Immunostaining for CD34 highlighted the rich vascular network (C) and stromal cells showed immunoreactivity for neuron specific enolase (D).

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